Adult onset still disease associated with endogenous lipoid pneumonia

Sami, Ramin and Zohal, Mohammadali and Mohammadi, Forozan (2019) Adult onset still disease associated with endogenous lipoid pneumonia. Advances in Respiratory Medicine.

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Cholesterol pneumonia or endogenous lipid pneumonia (ELP) is a rare disease that can occur in the context of a systemic disease or following a bronchial obstruction. It is characterized by a wide range of diverse symptoms and various disease course. The present report introduces a young woman diagnosed with adult onset still disease three years ago, who has been referred with macrophage activation syndrome (MAS). She underwent biopsy due to dyspnea and a crazy paving pattern in HRCT of the lungs, leading to the diagnosis of lipoid pneumonia based on the interstitial lymphocytic inflammation and cholesterol granulomas. So far, there has been no report indicating MAS associated with cholesterol pneumonia. This is the second case reporting ELP in the adult onset still disease. Key words: endogenous lipoid pneumonia; cholesterol pneumonia; adult onset still disease

Item Type: Article
Subjects: R Medicine > R Medicine (General)
Divisions: University Portal > research center > Metabolic
Depositing User: pr Metabolic diseases research
Date Deposited: 07 Nov 2022 10:58
Last Modified: 07 Nov 2022 10:58
URI: http://eprints.qums.ac.ir/id/eprint/12146

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